Additional pediatric resources: GeneralPediatrics.com | PediatricEducation.org | SearchingPediatrics.com
Michael P. D'Alessandro, M.D.
Peer Review Status: Internally Peer Reviewed
Etiology/Pathophysiology:
Congenital hamartomatous lesion of the lung.
Pathology:
There are 3 subtypes, all of which lack normal bronchial
communications:
Type I - multiple large air or fluid filled cysts, usually greater
than 2.0 cm in diameter
.
Type II - variably sized less bulky lesion with smaller cysts
.
Type III - bulky mass composed of multiple tiny, microscopic cysts
resembling bronchi that involves the entire lobe
. Adenomatous hyperplasia with an increase
in terminal bronchiolar structures, as well as a polypoid arrangement
of mucosal epithelium is seen.
Imaging Findings:
Seen with equal frequency in any lobe. Can rarely be bilateral
.
Type I - multiple large air or fluid filled cysts that produces a
mediastinal shift and compression of adjacent lung.
The most common type is Type I. It may
have air fluid levels in its cysts. If infected, it may appear
homogeneously opacified.
Type II - variable sized less bulky lesion with smaller cysts with less mediastinal shift and respiratory distress.
Type III - bulky radiographically solid mass composed of multiple tiny cysts that involves the entire lobe.
DDX:
References:
Additional pediatric resources: GeneralPediatrics.com | PediatricEducation.org | SearchingPediatrics.com
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