Michael P. D'Alessandro, M.D.
Peer Review Status: Internally Peer Reviewed
The patient was an 11 year old male with a long-standing history of plexiform neurofibromatosis involving his right arm and chest. His past surgical history was remarkable for having multiple resections of benign neurofibromas in the past.
Clinical Physical Exam:
Remarkable for an extensive soft tissue mass involving his right arm and chest.
Clinical Differential Diagnosis:
Spinal films and a chest CT exam demonstrated the extent of the right thoracic mass and its bony involvement.
Images 2 and 3
Imaging Differential Diagnosis:
Probably malignant degeneration of the plexiform neurofibroma due to its rapid increase in size.
The patient underwent elective resection of the large right posterior mediastinal mass. During the thoracotomy, the large mass was seen to originate in the apex of the right chest.
Examination of the surgical specimen revealed characteristic findings of malignant schwannoma within a plexiform neurofibroma.
Neurofibroma of Thorax
Follow-up and Prognosis:
The patient had an uncomplicated post-operative course.
Case 15, Case 18, Case 27, Case 46, Case 67, Case 69
Follow us on Twitter @pedseducation and @pedsimaging and Facebook @pedsimaging and Instagram @pedsimaging
Please send us comments by filling out our Comment Form.
All contents copyright © 1992-2016 Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D. and the authors. All rights reserved.
"Virtual Pediatric Hospital", the Virtual Pediatric Hospital logo, and "A digital library of pediatric information" are all Trademarks of Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D.
Virtual Pediatric Hospital is funded in whole by Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D. Advertising is not accepted.
Your personal information remains confidential and is not sold, leased, or given to any third party be they reliable or not.
The information contained in Virtual Pediatric Hospital is not a substitute for the medical care and advice of your physician. There may be variations in treatment that your physician may recommend based on individual facts and circumstances.