Michael P. D'Alessandro, M.D.
Peer Review Status: Internally Peer Reviewed
Is premature closure of a suture. Can be either primary (idiopathic) or secondary (due to skeletal dysplasias and syndromes, metabolic disease, hematologic disorders, ventricular shunting, and miscellaneous malformations). The primary ones develop in utero and are apparent at birth or shortly thereafter. There is a 3:1 male predominance.
The skull is altered in shape. The involved suture may appear narrowed, demonstrate parasutural sclerosis, sharpening and straightening of the sutural edges, and development of bony bridges. There may be partial or complete fusion of a suture, but a short segment of synostosis often produces the same deformity as a complete fusion. Multiple sutures are involved 11% of time. Plain films detect 89% of craniosynostosis while CT detects 94% of craniosynostosis.
Sagittal craniosynostosis (dolichocephaly, scaphocephaly) accounts for 56% of cases and has an elongated cranial vault.
Unilateral coronal synostosis (plagiocephaly) accounts for 11% of cases and has a harlequin appearance to the affected orbit.
Bilateral coronal synostosis (brachycephaly) accounts for 11% of cases and has a shortened, widened cranial vault and has a harlequin appearance to both orbits.
Metopic craniosynostosis accounts for 7% of cases, and lambdoid craniosynostosis accounts for 1% of cases.
See References Chapter.
Section Top | Title Page
Follow us on Twitter @pedseducation and @pedsimaging and Facebook @pedsimaging and Instagram @pedsimaging
Please send us comments by filling out our Comment Form.
All contents copyright © 1992-2016 Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D. and the authors. All rights reserved.
"Virtual Pediatric Hospital", the Virtual Pediatric Hospital logo, and "A digital library of pediatric information" are all Trademarks of Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D.
Virtual Pediatric Hospital is funded in whole by Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D. Advertising is not accepted.
Your personal information remains confidential and is not sold, leased, or given to any third party be they reliable or not.
The information contained in Virtual Pediatric Hospital is not a substitute for the medical care and advice of your physician. There may be variations in treatment that your physician may recommend based on individual facts and circumstances.