Virtual Pediatric Hospital(tm) : A digital library of pediatric information

Home | About | FAQ | Reviews | Search

Virtual Pediatric Hospital: Paediapaedia: Arnold Chiari Malformation Paediapaedia: Neurological Diseases

Arnold Chiari Malformation

Michael P. D'Alessandro, M.D.
Peer Review Status: Internally Peer Reviewed

Clinical Presentation:
Spinal deformity.

Is downward displacement of the cerebellum and fourth ventricle into the cervical canal and is part of the meningomyelocele complex.

Not applicable

Imaging Findings:
All types have hydrocephalus that is frequently asymmetric with disproportionate dilation of the occipital horns and atria relative to the frontal and temporal horns. There is a characteristic anterior pointing and medial concavity of the frontal horns, seen on the coronal scans. The massa intermedia is enlarged. The posterior fossa is relatively small. The interhemispheric fissue is sometimes prominent.

Type I - elongation and minimal displacement of the cerebellar tonsils inferiorly.

Type II - marked spinal herniation of the inferior cerebellar vermis, medulla oblongata, lower pons and fourth ventricle. In a newborn Type II is the most common and is nearly always associated with a meningomyelocele.

Type III - displacement of the entire cerebellum into a large cervical spina bifida.

Type IV - isolated cerebellar hypoplasia without significant displacement of posterior fossa contents.


See References Chapter.

Section Top | Title Page

Additional pediatric resources: | Facebook iconTwitter iconRSS icon |

Follow us on Twitter @pedseducationTwitter icon and @pedsimagingTwitter icon and Facebook @pedsimagingFacebook icon and Instagram @pedsimagingInstagram icon

About Us | FAQ | Reviews | Contact Us | Search

Virtual Pediatric Hospital is curated by Donna M. D'Alessandro, M.D. and by Michael P. D'Alessandro, M.D.

Please send us comments by filling out our Comment Form.

All contents copyright © 1992-2016 Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D. and the authors. All rights reserved.

"Virtual Pediatric Hospital", the Virtual Pediatric Hospital logo, and "A digital library of pediatric information" are all Trademarks of Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D.

Virtual Pediatric Hospital is funded in whole by Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D. Advertising is not accepted.

Your personal information remains confidential and is not sold, leased, or given to any third party be they reliable or not.

The information contained in Virtual Pediatric Hospital is not a substitute for the medical care and advice of your physician. There may be variations in treatment that your physician may recommend based on individual facts and circumstances.