Virtual Pediatric Hospital(tm) : A digital library of pediatric information

Home | About | FAQ | Reviews | Search

Virtual Pediatric Hospital: Paediapaedia: Pulmonary Lymphangiectasia Paediapaedia: Neonatal Chest Diseases

Pulmonary Lymphangiectasia

Michael P. D'Alessandro, M.D.
Peer Review Status: Internally Peer Reviewed

Clinical Presentation:
Respiratory distress in a newborn.

Complete pulmonary venous atresia leads to pulmonary venous obstruction which results in engorged pulmonary lymphatics and capillaries. Heart size is normal since flow through the left side of the heart is decreased. The condition usually is fatal. It is classified into 3 types: (1) Pulmonary lymphangiectasia associated with congenital heart lesions characterized by obstruction of pulmonary venous return [totally anomalous venous return below the diaphragm, pulmonary venous atresia, mitral atresia, hypoplastic left heart], (2) Pulmonary lymphangiectasia associated with systemic lymphangiectasia, and (3) Isolated pulmonary lymphangiectasia. Type (1) is the most common, Type (3) is the rarest.

Absence of the pulmonary venous structures, prominence of the pulmonary lymphatics and capillaries.

Imaging Findings:
Prominent bilateral, symmetrical interstitial distention of lymphatics with a general branching pattern radiating from the hila that extends to the periphery with prominence of Kerley B lines. icon gif Diffuse pulmonary hyperinflation is also seen. Less commonly a ground glass pattern can be seen.


See References Chapter.

Section Top | Title Page

Additional pediatric resources: | Facebook iconTwitter iconRSS icon |

Follow us on Twitter @pedseducationTwitter icon and @pedsimagingTwitter icon

About Us | FAQ | Reviews | Contact Us | Search

Virtual Pediatric Hospital is curated by Donna M. D'Alessandro, M.D. and by Michael P. D'Alessandro, M.D.

Please send us comments by filling out our Comment Form.

All contents copyright © 1992-2016 Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D. and the authors. All rights reserved.

"Virtual Pediatric Hospital", the Virtual Pediatric Hospital logo, and "A digital library of pediatric information" are all Trademarks of Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D.

Virtual Pediatric Hospital is funded in whole by Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D. Advertising is not accepted.

Your personal information remains confidential and is not sold, leased, or given to any third party be they reliable or not.

The information contained in Virtual Pediatric Hospital is not a substitute for the medical care and advice of your physician. There may be variations in treatment that your physician may recommend based on individual facts and circumstances.