Virtual Pediatric Hospital(tm) : A digital library of pediatric information

Home | Search | About Us | FAQ | Reviews | Contact Us
Follow us on Twitter @pedseducationTwitter icon and @pedsimagingTwitter icon

Additional pediatric resources: SearchingPediatrics.com | PediatricEducation.org Facebook iconTwitter iconRSS icon | GeneralPediatrics.com | Pediatric Commons


Virtual Pediatric Hospital: Paediapaedia: Choledochal Cyst Paediapaedia: Gastrointestinal Diseases

Choledochal Cyst

Michael P. D'Alessandro, M.D.
Peer Review Status: Internally Peer Reviewed


Clinical Presentation:
The classic clinical triad, which is seen in 25% of patients is jaundice, abdominal pain, and a right upper quadrant mass. Fifty percent of patients present by 10 years old.

Etiology/Pathophysiology:
A focal dilatation of the common and hepatic bile ducts of unknown etiology. Type 1 is the most common. Type 1A is dilation of the common bile duct below the cystic duct, Type 1B is dilation of the common and hepatic ducts. Type 2 is focal eccentric dilation of the common bile duct. Type 3 is a distal dilation of the common bile duct within the wall of the duodenum, a choledochocele. Caroli's disease, which is a cystic dilation of the intra and extrahepatic biliary ducts is sometimes classified as a Type 4 but is not really related to choledochal cyst. Complications include biliary cirrhosis and portal hypertension from prolonged extrahepatic obstruction, cyst rupture, stone formation, and cancer late in life.

Pathology:
Not applicable

Imaging Findings:
Ultrasound shows a large cystic lesion in the porta hepatis that is distinct from the gallbladder and communicates with dilated intrahepatic biliary ducts. DISIDA demonstrates normal hepatic extratction of tracer, excretion of tracer into the biliary system, and accumulation of tracer in the cyst.

DDX:

References:
See References Chapter.

Section Top | Title Page


Follow us on Twitter @pedseducationTwitter icon and @pedsimagingTwitter icon

Additional pediatric resources: SearchingPediatrics.com | PediatricEducation.org Facebook iconTwitter iconRSS icon | GeneralPediatrics.com | Pediatric Commons


Home | Search | About Us | FAQ | Reviews | Contact Us

Virtual Pediatric Hospital is curated by Donna M. D'Alessandro, M.D. [Google+ Profile] and by Michael P. D'Alessandro, M.D.

Please send us comments by filling out our Comment Form.

All contents copyright 1992-2014 Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D. and the authors. All rights reserved.

"Virtual Pediatric Hospital", the Virtual Pediatric Hospital logo, and "A digital library of pediatric information" are all Trademarks of Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D.

Virtual Pediatric Hospital is funded in whole by Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D. Advertising is not accepted.

Your personal information remains confidential and is not sold, leased, or given to any third party be they reliable or not.

The information contained in Virtual Pediatric Hospital is not a substitute for the medical care and advice of your physician. There may be variations in treatment that your physician may recommend based on individual facts and circumstances.

URL: http://www.virtualpediatrichospital.org/

This website is certified by Health On the Net Foundation. Click to verify. This site complies with the HONcode standard for trustworthy health information:
verify here.