Virtual Pediatric Hospital(tm) : A digital library of pediatric information

Home | About | FAQ | Reviews | Search

Virtual Pediatric Hospital: Paediapaedia: Pulmonary Arteriovenous Malformation (AVM) Paediapaedia: Chest and Airway Diseases

Pulmonary Arteriovenous Malformation (AVM)

Michael P. D'Alessandro, M.D.
Peer Review Status: Internally Peer Reviewed

Clinical Presentation:
Twenty-five percent have symptoms including cyanosis, dyspnea, and easy fatigability. There may be a machinery murmur, especially on inspiration. Fifty percent have telangiectasias on the mucous membranes and skin - especially in familial hemorrhagic telangiectasis (Osler-Weber Rendu).

A congenital malformation resulting in direct intrapulmonary connections between the pulmonary arteries and veins without an intervening capillary bed. This causes a right to left shunt with peripheral arterial oxygen desaturation. Brain abscesses can develop due to lack of pulmonary capillary filtration of microorganisms.

Not applicable

Imaging Findings:
Sixty-five percent are single, 75% are unilateral, and 60% are in the lower lobes usually right beneath the visceral pleura. On CXR a soft tissue mass is seen in the lung that may have tubular densities (vein and artery) connecting it to the hilum. Pulmonary angiography is diagnostic and is used to define the number, size and location of the fistulae.


See References Chapter.

Section Top | Title Page

Additional pediatric resources: | Facebook iconTwitter iconRSS icon |

Follow us on Twitter @pedseducationTwitter icon and @pedsimagingTwitter icon and Facebook @pedsimagingFacebook icon and Instagram @pedsimagingInstagram icon

About Us | FAQ | Reviews | Contact Us | Search

Virtual Pediatric Hospital is curated by Donna M. D'Alessandro, M.D. and by Michael P. D'Alessandro, M.D.

Please send us comments by filling out our Comment Form.

All contents copyright © 1992-2016 Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D. and the authors. All rights reserved.

"Virtual Pediatric Hospital", the Virtual Pediatric Hospital logo, and "A digital library of pediatric information" are all Trademarks of Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D.

Virtual Pediatric Hospital is funded in whole by Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D. Advertising is not accepted.

Your personal information remains confidential and is not sold, leased, or given to any third party be they reliable or not.

The information contained in Virtual Pediatric Hospital is not a substitute for the medical care and advice of your physician. There may be variations in treatment that your physician may recommend based on individual facts and circumstances.