Virtual Pediatric Hospital(tm) : A digital library of pediatric information

Home | About | FAQ | Reviews | Search

Virtual Pediatric Hospital: Paediapaedia: Totally Anomalous Pulmonary Venous Return, Infradiaphragmatic (TAPVR) Paediapaedia: Cardiovascular Diseases

Totally Anomalous Pulmonary Venous Return, Infradiaphragmatic (TAPVR)

Michael P. D'Alessandro, M.D.
Peer Review Status: Internally Peer Reviewed

Clinical Presentation:
Presents with dyspnea and cyanosis that is progressive and that is increased with crying and feeding due to esophageal compression of the common venous channel as it passes through the esophageal hiatus.

The pulmonary venous drainage goes from the common pulmonary vein to the vertical retrocardiac pulmonary vein which goes through the esophageal hiatus to empty into the ductus venosus / portal vein / tributary of the portal vein. This causes a relative obstruction to pulmonary venous drainage and results in pulmonary venous hypertension. There is diminished blood flow to the left side of heart and to the right side of the heart so there is no volume overload and no cardiac enlargement.

Not applicable

Imaging Findings:
On CXR there is obvious pulmonary venous hypertension and edema, but no cardiomegaly. An esophagram can show an anterior impression on a barium filled esophagus by a retrocardiac common pulmon vein.

Pulmonary venous hypertension with cardiomegaly

See References Chapter.

Section Top | Title Page

Additional pediatric resources: | Facebook iconTwitter iconRSS icon |

Follow us on Twitter @pedseducationTwitter icon and @pedsimagingTwitter icon

About Us | FAQ | Reviews | Contact Us | Search

Virtual Pediatric Hospital is curated by Donna M. D'Alessandro, M.D. and by Michael P. D'Alessandro, M.D.

Please send us comments by filling out our Comment Form.

All contents copyright © 1992-2016 Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D. and the authors. All rights reserved.

"Virtual Pediatric Hospital", the Virtual Pediatric Hospital logo, and "A digital library of pediatric information" are all Trademarks of Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D.

Virtual Pediatric Hospital is funded in whole by Donna M. D'Alessandro, M.D. and Michael P. D'Alessandro, M.D. Advertising is not accepted.

Your personal information remains confidential and is not sold, leased, or given to any third party be they reliable or not.

The information contained in Virtual Pediatric Hospital is not a substitute for the medical care and advice of your physician. There may be variations in treatment that your physician may recommend based on individual facts and circumstances.