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Virtual Pediatric Hospital: Paediapaedia: Hypoplastic Right Heart Disease Paediapaedia: Cardiovascular Diseases

Hypoplastic Right Heart Disease (Pulmonary Atresia)

Michael P. D'Alessandro, M.D.
Peer Review Status: Internally Peer Reviewed

Clinical Presentation:
The patients are cyanotic at birth and get more hypoxic as the ductus arteriosus closes.

This consists of a complete obstruction of the right ventricle outflow tract due to a hypoplastic pulmonary artery. When the ventricular septum is intact a patent foramen ovale is the site of the right to left shunt with a PDA and / or bronchial collateral arteries providing the only source of pulmonary blood flow. There are two types:

Not applicable

Imaging Findings:
On CXR decreased pulmonary vasculature and cardiomegaly is seen.

Cardiomegaly and decreased pulmonary vasculature:

See References Chapter.

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